Children with cholestatic liver diseases (CLD) have unique nutritional requirements. Without bile reaching their intestines, they often suffer from fat-malabsorption and associated consequences. As a result, they require specialize formulas, as well as intensive nutrition monitoring.
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This webinar, developed by GI Kids and The NASPGHAN Foundation, discusses nutritional considerations in children with cholestasis, with emphasis on nutritional support and vitamin/micronutrient deficiencies. The webinar was supported by an educational grant from Albireo Pharma.
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// VIDEO CHAPTERS //
1:11 Meet Dr. Shikha Sundaram, MD, Associate Professor of Pediatrics at University of Colorado School of Medicine, Aurora, CO
2:08 Nutritional Management of Children with Cholestatic Liver Disease (CLD): Introduction, Example Clinical Case and Webinar Objectives
4:28 Pathophysiology of Malnutrition
6:16 Assessing Nutritional Status of Patients through Physical Exams
9:32 Physical Exam Clues of Deficiencies Indicating Liver Disease
10:24 How Frailty Measurement May Help to Better Differentiate Nutrition and Malnutrition in Children with CLD
13:09 How CT/MRI Imaging May Help to Better Assess Nutrition and Malnutrition in Patients
14:51 Determining Macronutrient Needs for Patients
17:15 Practical Approaches to Feeding Children with End Stage Liver Disease
19:49 How to Care for the Patient with CLD after Completing Assessment of Patient Nutritional Status
21:09 Meet Dr. Jennifer Vittorio, MD, Assistant Professor of Pediatrics, Columbia University, New York, NY
22:32 Pediatric Cholestasis: Fat-soluble Vitamin Deficiencies and Available Treatments Introduction and Objectives of Presentation
23:16 Definition and Overview of Cholestasis
24:11 Fat-soluble Vitamins and Common Nutritional Deficiencies in Children with CLD
25:49 Severity of Fat-soluble Vitamin Deficiencies
27:23 Initial Supplementation: AQUADEKS
27:52 Additional Treatment Strategies
30:32 Role of Fat-soluble Vitamins in Nutrition, Assessment Vitamin Levels in Patients and Supplementation Strategies
43:03 Treatment Approach for Example Clinical Case and Presentation Summary
43:45 References for Dr. Jennifer Vittorio, MD, presentation
44:03 Q&A
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